Neuronal ceroid-lipofuscinoses
URI(s)
- http://id.loc.gov/authorities/subjects/sh85091152
- info:lc/authorities/sh85091152
- http://id.loc.gov/authorities/sh85091152#concept
Instance Of
Scheme Membership(s)
Collection Membership(s)
Variants
- Batten-Spielmeyer-Vogt disease
- Batten's disease
- Ceroid-lipofuscinoses, Neuronal
- Jansky-Bielschowsky disease
- Kufs disease
- Lipofuscinoses, Neuronal ceroid
- Neuronal ceroid-lipofuscinosis
- Santavuori-Haltia disease
- Spielmeyer-Sjogren disease
- Spielmeyer-Vogt disease
- Vogt Spielmeyer disease
Broader Terms
Closely Matching Concepts from Other Schemes
Earlier Established Forms
- Neuronal ceroid-lipofuscinosis
Sources
- found: MeSH, June 12, 2018Neuronal ceroid-lipofuscinoses (A group of severe neurodegenerative diseases characterized by intracellular accumulation of autofluorescent wax-like lipid materials (CEROID; LIPOFUSCIN) in neurons. Entry terms (abbreviated list): Batten-Spielmeyer-Vogt disease, Batten's disease, Jansky-Bielschowsky disease, Kufs disease, Santavuori-Haltia disease, Spielmeyer-Sjogren disease, Spielmeyer-Vogt disease, Vogt Spielmeyer disease. Mapped to: Neurodegenerative diseases; Genetic diseases, Inborn; Metabolism, Inborn errors; Lipidoses)
LC Classification
- RC632.N47
Change Notes
- 1986-02-11: new
- 2018-07-13: revised
Alternate Formats
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